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β4GALT1-CDG uncovers a novel mechanism of Von Willebrand factor deficiency through impaired glycosylation and accelerated
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Interferences by factor VIII and lupus anticoagulant in the modified one‐stage assay for emicizumab
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Emicizumab does not interfere with the activated clotting time
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Antithrombotic potential of a single‐domain antibody enhancing the activated protein C‐cofactor activity of protein S
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Pathophysiological pathway differences in children who present with COVID-19 ARDS compared to COVID -19 induced MIS-C
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Emicizumab does not interfere with the activated clotting time
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The Proteolytic Inactivation of Protein Z-Dependent Protease Inhibitor by Neutrophil Elastase Might Promote the Procoagulant Activity of Neutrophil Extracellular Traps in Sepsis
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Assessing bleeding risk in 18 children with Osteogenesis imperfecta
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Long-Term Follow-up Study after Lentiviral Hematopoietic Stem/Progenitor Cell Gene Therapy for Wiskott - Aldrich Syndrome
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Serpins in Hemostasis as Therapeutic Targets for Bleeding or Thrombotic Disorders
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Anti-inflammatory Activity of the Protein Z-Dependent Protease Inhibitor
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Clinical variability and probable founder effect in oculocutaneous albinism type 7.
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International clinical guidelines for the management of phosphomannomutase 2‐congenital disorders of glycosylation: Diagnosis, treatment and follow up
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Article dans une revue
(article de synthèse)
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Impact of Heparin- or Nonheparin-Coated Circuits on Platelet Function in Pediatric Cardiac Surgery
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Article dans une revue
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An ADAM-10 dependent EPCR shedding links meningococcal interaction with endothelial cells to purpura fulminans
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Article dans une revue
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TUBB1 mutations cause thyroid dysgenesis associated with abnormal platelet physiology
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Article dans une revue
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A mutation in the gene coding for the sialic acid transporter SLC35A1 is required for platelet life span but not proplatelet formation
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Article dans une revue
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Inactivated antithombin as anticoagulant reversal in a rat model of cardiopulmonary bypass: a potent and potentially safer alternative to protamine
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Complex formation with pentraxin-2 regulates factor X plasma levels and macrophage interactions
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Pathogenesis of meningococcal purpura fulminans
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Article dans une revue
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Targeting VEGFR1 on endothelial progenitors modulates their differentiation potential
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