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The beneficial effect of chronic muscular exercise on muscle fragility is increased by Prox1 gene transfer in dystrophic mdx muscle
Alexandra Monceau
,
Clément Delacroix
,
Mégane Lemaitre
,
Gaelle Revet
,
Denis Furling
Article dans une revue
hal-03830867v1
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Reversal of RNA toxicity in myotonic dystrophy via a decoy RNA-binding protein with high affinity for expanded CUG repeats
Ludovic Arandel
,
Magdalena Matloka
,
Arnaud F Klein
,
Frédérique Rau
,
Alain Sureau
Article dans une revue
hal-03830811v1
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Dystrophin Restoration after Adeno-Associated Virus U7–Mediated Dmd Exon Skipping Is Modulated by Muscular Exercise in the Severe D2-Mdx Duchenne Muscular Dystrophy Murine Model
Alexandra Monceau
,
Dylan Moutachi
,
Mégane Lemaitre
,
Luis Garcia
,
Capucine Trollet
Article dans une revue
hal-03830848v1
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Comprehensive transcriptome-wide analysis of spliceopathy correction of myotonic dystrophy using CRISPR-Cas9 in iPSCs-derived cardiomyocytes
Sumitava Dastidar
,
Debanjana Majumdar
,
Jaitip Tipanee
,
Kshitiz Singh
,
Arnaud Klein
Article dans une revue
hal-03410645v1
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Desmin prevents muscle wasting, exaggerated weakness and fragility, and fatigue in dystrophic mdx mouse
Arnaud Ferry
,
Julien Messéant
,
Ara Parlakian
,
Mégane Lemaitre
,
Pauline Roy
Article dans une revue
hal-02996889v1
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Peptide-conjugated oligonucleotides evoke long-lasting myotonic dystrophy correction in patient-derived cells and mice
Arnaud F Klein
,
Miguel A Varela
,
Ludovic Arandel
,
Ashling Holland
,
Naira Naouar
Article dans une revue
hal-03753531v1
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Genome Editing of Expanded CTG Repeats within the Human DMPK Gene Reduces Nuclear RNA Foci in the Muscle of DM1 Mice
Mirella Lo Scrudato
,
Karine Poulard
,
Célia Sourd
,
Stéphanie Tomé
,
Arnaud Klein
Article dans une revue
hal-02177548v1
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Cells of Matter—In Vitro Models for Myotonic Dystrophy
Magdalena Matloka
,
Arnaud F Klein
,
Frédérique Rau
,
Denis Furling
Article dans une revue
hal-03830776v1
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Improvement of Dystrophic Muscle Fragility by Short-Term Voluntary Exercise through Activation of Calcineurin Pathway in mdx Mice
Clement Delacroix
,
Janek Hyzewicz
,
Megane Lemaitre
,
Bertrand Friguet
,
Zhenlin Li
Article dans une revue
hal-02134917v1
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Efficient CRISPR/Cas9-mediated editing of trinucleotide repeat expansion in myotonic dystrophy patient-derived iPS and myogenic cells
Sumitava Dastidar
,
Simon Ardui
,
Kshitiz Singh
,
Debanjana Majumdar
,
Nisha Nair
Article dans une revue
hal-02357315v1
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Immortalized human myotonic dystrophy muscle cell lines to assess therapeutic compounds
Ludovic Arandel
,
Micaela Polay Espinoza
,
Magdalena Matloka
,
Audrey Bazinet
,
Damily de Dea Diniz
Article dans une revue
hal-01519721v1
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Two novel COLVI long chains in zebrafish that are essential for muscle development
Laetitia Ramanoudjame
,
Claire Rocancourt
,
Jeanne Lainé
,
Arnaud Klein
,
Lucette Joassard
Article dans une revue
hal-01594462v1
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New function for the RNA helicase p68/DDX5 as a modifier of MBNL1 activity on expanded CUG repeats
François-Xavier Laurent
,
Alain Sureau
,
Arnaud F Klein
,
François Trouslard
,
Erwan Gasnier
Article dans une revue
hal-03001690v1
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Selective silencing of mutated mRNAs in DM1 by using modified hU7-snRNAs
Virginie François
,
Arnaud F Klein
,
Cyriaque Beley
,
Arnaud Jollet
,
Camille Lemercier
Article dans une revue
hal-03002664v1
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Misregulated alternative splicing of BIN1 is associated with T tubule alterations and muscle weakness in myotonic dystrophy.
Charlotte Fugier
,
Arnaud F Klein
,
Caroline Hammer
,
Stéphane Vassilopoulos
,
Ylva Ivarsson
Article dans une revue
hal-00811986v1
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PABPN1 polyalanine tract deletion and long expansions modify its aggregation pattern and expression
Arnaud F Klein
,
Mitsuru Ebihara
,
Christine Alexander
,
Marie-Josée Dicaire
,
A. Marie-Josée Sasseville
Article dans une revue
hal-03821688v1
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PABPN1 overexpression leads to upregulation of genes encoding nuclear proteins that are sequestered in oculopharyngeal muscular dystrophy nuclear inclusions
Louis-Philippe Corbeil-Girard
,
Arnaud F Klein
,
A. Marie-Josée Sasseville
,
Hugo Lavoie
,
Anik Saint-Denis
Article dans une revue
hal-03832516v1
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